A RARE PRESENTATION OF EWING SACROMA AS A PRIMARY INTRADURAL EXTRAMEDULLARY MASS IN PAEDIATRIC PATIENT

Received 2023-11-11; Accepted 2024-05-03; Published 2024-10-17

Authors

  • Jun Kai Lee Department of Radiology, School of Medical Sciences, Health Campus, Universiti Sains Malaysia, 16150 Kubang Kerian, Kelantan, Malaysia.
  • Noor Khairiah A. Karim Department of Biomedical Imaging, Advanced Medical and Dental Institute, Universiti Sains Malaysia, Bertam, 13200 Kepala Batas, Pulau Pinang, Malaysia.
  • Lee Nah Ang Department of Radiology, Hospital Pulau Pinang, 10990 George Town, Pulau Pinang, Malaysia.
  • Yann Tyng Chau Department of Pathology, Hospital Pulau Pinang, 10990 George Town, Pulau Pinang, Malaysia.

DOI:

https://doi.org/10.22452/jummec.vol27no2.30

Keywords:

Ewing Sarcoma, Extra-skeletal Ewing Sarcoma, Intradural Extramedullary Ewing Sarcoma, Spinal Ewing Sarcoma, Magnetic Resonance Imaging

Abstract

Ewing sarcoma (ES) is a highly malignant bone tumor that accounts for 25% of all bone tumors in childhood. Primary spinal ES is very uncommon. Primary intradural extramedullary Ewing sarcoma (IEES) is even rarer, and high clinical suspicion is vital to guide accurate management and tissue diagnosis. A 10-year-old boy presented with a 3-week history of non-specific back pain, which worsened and impaired his regular activities. Urgent magnetic resonance imaging (MRI) revealed a thoracic intradural extramedullary mass causing regional compression. Tumor debulking surgery was performed, and histopathological examination of the excised mass was consistent with ES. Early recognition and management of highly aggressive tumors are essential, more so in critical regions such as the spine. Our case emphasises the need to consider ES as a differential diagnosis for spinal tumors in intradural extramedullary locations in the pediatric age group, as the aim of treatment should be curative and not palliative due to high 5-year survivability.

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Published

2024-10-17

Issue

Vol. 27 No. 2 (2024)

Section

Research article

License

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